A Strategic Approach To Combat Haemophilia –A During Emergencies

Abstract

Background : Haemophilia –A  is an  X-linked recessive inherited  bleeding  disorder due to a deficiency of coagulation  factor- VIII resulting in increased mortality  and  morbidity¹.It  has  an estimated frequency of approximately one in 10,000 live births  affecting mostly the males  while the females are considered as  carriers of haemophilia².

Aim :  The purpose of the report is to present the evidence of a known haemophilia –A male patient  who suffered from the consequences of an emergency ( road accident ).

Methodology: The familial history of the patient along with clinical manifestations was taken into account. Since he was a known case of haemophilic arthropathy, and a factor-VIII replacement was done as per the guidelines of World Federation of Haemophilia³. And the fracture of tibia was fixed with nailing and a good post-operative care was given.

Conclusion : The report concluded  that health care professionals combined strategies right from administering medical  treatment  to rendering surgical support and it underlined the fact  that  with the timely medical intervention, the complications of haemophilia-A could be successfully managed.